Cystic Fibrosis - Page 5

Artigo Original Capacidade submáxima de exercício em pacientes adolescentes e adultos com fibrose cística* Submaximal exercise capacity in adolescent and adult patients with cystic fibrosis

Cystic Fibrosis / Nutritional Status / Body Mass Index / Physical Impairment / Forced Vital Capacity / Pulmonary Function / Pulmonary function test / Cross sectional Study / Exercise Tolerance / Oxygen saturation / Clinical evaluation / Chest X-ray / Pulmonary Function / Pulmonary function test / Cross sectional Study / Exercise Tolerance / Oxygen saturation / Clinical evaluation / Chest X-ray

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Polimorfismo de los genes mucA y fpvA en Pseudomonas aeruginosa de pacientes con fibrosis quística: coexistencia de variantes genéticas en el mismo paciente

Cystic Fibrosis / Medical Microbiology / Adolescent / Humans / Child / Female / Male / Young Adult / Pseudomonas aeruginosa / Adult / Genetic variation / Pseudomonas Aeruginosa / Female / Male / Young Adult / Pseudomonas aeruginosa / Adult / Genetic variation / Pseudomonas Aeruginosa

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Asociación entre colonización-infección crónica por Pseudomonas aeruginosa e hiperreactividad bronquial en pacientes con fibrosis quística

Cystic Fibrosis / Arch / Pseudomonas aeruginosa / Clinical Sciences / Pseudomonas Aeruginosa

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GSH monoethyl ester rescues mitochondrial defects in cystic fibrosis models

Genetics / Cystic Fibrosis / Mitochondria / Biological Sciences / Cell line / Models / Mutation / Mice / Animals / Male / Human Molecular Genetics / Glutathione / Membrane transport proteins / Interleukin / Models / Mutation / Mice / Animals / Male / Human Molecular Genetics / Glutathione / Membrane transport proteins / Interleukin

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Transient exocrine pancreatic insufficiency as a possible complication of an enterovirus infection

Cystic Fibrosis / Pancreatitis / Diarrhea / Humans / Child / Male / Differential Diagnosis / Acute Pancreatitis / Chronic Pancreatitis / Public health systems and services research / Viral Infection / Exocrine Pancreatic Insufficiency / Male / Differential Diagnosis / Acute Pancreatitis / Chronic Pancreatitis / Public health systems and services research / Viral Infection / Exocrine Pancreatic Insufficiency

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Endoscopic treatment of paranasal sinus mucoceles in children

Magnetic Resonance Imaging / Cystic Fibrosis / Endoscopy / Humans / Child / Female / Male / Paranasal Sinuses / Clinical Sciences / X ray Computed Tomography / Endoscopic Sinus Surgery / Female / Male / Paranasal Sinuses / Clinical Sciences / X ray Computed Tomography / Endoscopic Sinus Surgery

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Successful transplantation of B. cepacia complex infected cystic fibrosis patients; transplanting B. cenocepacia (genomovar III) infected patients

Cystic Fibrosis / Heart and Lung Transplantation

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Burkholderia cenocepacia J2315 acyl carrier protein: A potential target for antimicrobials\' development?

Microbiology / Immunology / Biofilms / Caenorhabditis elegans / Cystic Fibrosis / Medical Microbiology / Virulence / Humans / Models / Biofilm / Sequence alignment / Mutation / Escherichia coli / Animals / Bacteria / Microbial / Microbial Pathogenesis / Fatty Acid / Amino Acid Profile / Molecular Mass / Antibacterial Agent / Amino Acid Sequence / Cell Surface Markers / Burkholderia Cepacia Complex / Medical Microbiology / Virulence / Humans / Models / Biofilm / Sequence alignment / Mutation / Escherichia coli / Animals / Bacteria / Microbial / Microbial Pathogenesis / Fatty Acid / Amino Acid Profile / Molecular Mass / Antibacterial Agent / Amino Acid Sequence / Cell Surface Markers / Burkholderia Cepacia Complex

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Efectividad en la aplicación de tres protocolos de prevención y tratamiento de la osteoporosis en pacientes adultos con fibrosis quística

Cystic Fibrosis / Vitamin D / Bone Mineral Density / Medicina Clinica

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Bactericidal efficacy of liposomal aminoglycosides against Burkholderia cenocepacia

Microbiology / Flow Cytometry / Cystic Fibrosis / Medical Microbiology / Transmission Electron Microscopy / Drug Delivery System / Pharmaceutical Chemistry / Stability / Antibiotic Resistance / Lipids / Humans / Cholesterol / Bacteria / Temperature / Liposomes / Aminoglycosides / Fusion / Antimicrobial chemotherapy / Immunochemistry / Anti-Bacterial Agents / Burkholderia / Microbial Sensitivity Tests / Mechanism of action / Microbial Viability / Drug Stability / Burkholderia Cepacia Complex / Drug Delivery System / Pharmaceutical Chemistry / Stability / Antibiotic Resistance / Lipids / Humans / Cholesterol / Bacteria / Temperature / Liposomes / Aminoglycosides / Fusion / Antimicrobial chemotherapy / Immunochemistry / Anti-Bacterial Agents / Burkholderia / Microbial Sensitivity Tests / Mechanism of action / Microbial Viability / Drug Stability / Burkholderia Cepacia Complex

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Superior vena cava obstruction due to total implantable venous access devices in cystic fibrosis: Case series and review

Respiratory Medicine / Cystic Fibrosis / cerebral Venous sinus thrombosis / Life Expectancy / Risk factors / Risk Factors / SUPERIOR VENA CAVA / Risk Factors / SUPERIOR VENA CAVA

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A broad spectrum of developmental delay in a large cohort of prolidase deficiency patients demonstrates marked interfamilial and intrafamilial phenotypic variability

Genetics / Family / Cystic Fibrosis / Humans / Child / Systemic Lupus Erythematosus / Mutation / Variability / Haplotypes / Female / Male / Cohort Study / Developmental disabilities / American / Gene / Pedigree / Phenotype / Clinical Sciences / Gen / Spectrum / Deficiency / Prenatal Diagnosis / Amino Acid Sequence / Base Sequence / Developmental delay / Deficit / Neurosciences / Founder Effect / Cohort Studies / Molecular Sequence Data / Systemic Lupus Erythematosus / Mutation / Variability / Haplotypes / Female / Male / Cohort Study / Developmental disabilities / American / Gene / Pedigree / Phenotype / Clinical Sciences / Gen / Spectrum / Deficiency / Prenatal Diagnosis / Amino Acid Sequence / Base Sequence / Developmental delay / Deficit / Neurosciences / Founder Effect / Cohort Studies / Molecular Sequence Data

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Burkholderia cenocepacia J2315 acyl carrier protein: A potential target for antimicrobials\' development?

Microbiology / Immunology / Biofilms / Caenorhabditis elegans / Cystic Fibrosis / Medical Microbiology / Virulence / Humans / Models / Biofilm / Sequence alignment / Mutation / Escherichia coli / Animals / Bacteria / Microbial / Microbial Pathogenesis / Fatty Acid / Amino Acid Profile / Molecular Mass / Antibacterial Agent / Amino Acid Sequence / Cell Surface Markers / Burkholderia Cepacia Complex / Molecular Sequence Data / Medical Microbiology / Virulence / Humans / Models / Biofilm / Sequence alignment / Mutation / Escherichia coli / Animals / Bacteria / Microbial / Microbial Pathogenesis / Fatty Acid / Amino Acid Profile / Molecular Mass / Antibacterial Agent / Amino Acid Sequence / Cell Surface Markers / Burkholderia Cepacia Complex / Molecular Sequence Data

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Oral miglustat in homozygous F508del CF patients

Cystic Fibrosis / Clinical Sciences

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Anticoncepción, embarazo y enfermedades respiratorias minoritarias

Contraception / Cystic Fibrosis / Risk / Pulmonary Hypertension / Genetic counseling / Pregnancy / Humans / Survivors / Female / Life Expectancy / High risk pregnancy / Clinical Sciences / Newborn Infant / Preimplantation genetic diagnosis / Cesarean Section / Heart and Lung Transplantation / Prenatal Care / Pregnancy / Humans / Survivors / Female / Life Expectancy / High risk pregnancy / Clinical Sciences / Newborn Infant / Preimplantation genetic diagnosis / Cesarean Section / Heart and Lung Transplantation / Prenatal Care

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A Complete Lipopolysaccharide Inner Core Oligosaccharide Is Required for Resistance of Burkholderia cenocepacia to Antimicrobial Peptides and Bacterial Survival In Vivo

Microbiology / Bacteriology / Cystic Fibrosis / Biological Sciences / Lipopolysaccharide / Virulence / Resistance / Animals / Bacteria / Peptides / Lung / Antimicrobial Peptide / Enzyme / Inner Core / Lipopolysaccharides / Anti-Bacterial Agents / Rats / Burkholderia / Rat Model / Oligosaccharides / Virulence / Resistance / Animals / Bacteria / Peptides / Lung / Antimicrobial Peptide / Enzyme / Inner Core / Lipopolysaccharides / Anti-Bacterial Agents / Rats / Burkholderia / Rat Model / Oligosaccharides

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