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Cystic Fibrosis
Cystic Fibrosis
Anticoncepción, embarazo y enfermedades respiratorias minoritarias
Contraception / Cystic Fibrosis / Risk / Pulmonary Hypertension / Genetic counseling / Pregnancy / Humans / Survivors / Female / Life Expectancy / High risk pregnancy / Clinical Sciences / Newborn Infant / Preimplantation genetic diagnosis / Cesarean Section / Heart and Lung Transplantation / Prenatal Care / Pregnancy / Humans / Survivors / Female / Life Expectancy / High risk pregnancy / Clinical Sciences / Newborn Infant / Preimplantation genetic diagnosis / Cesarean Section / Heart and Lung Transplantation / Prenatal Care
Interleukin-1β regulates CFTR expression in human intestinal T84 cells
Cystic Fibrosis / Inflammation / Gene expression / Protein Tyrosine Kinase / Clinical Sciences / Chloride Channel / Protein Expression / Autosomal Recessive / Biochemistry and cell biology / Chloride Channel / Protein Expression / Autosomal Recessive / Biochemistry and cell biology
Transfer of a cathelicidin peptide antibiotic gene restores bacterial killing in a cystic fibrosis xenograft model
Cystic Fibrosis / Humans / Animals / Clinical / Gene transfer techniques / Staphylococcus aureus / Cell Transplantation / Pseudomonas aeruginosa / Anti-Bacterial Agents / Antimicrobial Cationic Peptides / Chickens / Swine / HeLa cells / Pseudomonas Aeruginosa / Clinical Investigation / Staphylococcus aureus / Cell Transplantation / Pseudomonas aeruginosa / Anti-Bacterial Agents / Antimicrobial Cationic Peptides / Chickens / Swine / HeLa cells / Pseudomonas Aeruginosa / Clinical Investigation
Filovirus-pseudotyped lentiviral vector can efficiently and stably transduce airway epithelia in vivo
Cystic Fibrosis / Multidisciplinary / HIV / Dogs / Humans / Mice / Animals / Cell Polarity / Lung / Behavioral Animal Models / Epithelium / Respiratory System / Trachea / Filoviridae / Mice / Animals / Cell Polarity / Lung / Behavioral Animal Models / Epithelium / Respiratory System / Trachea / Filoviridae
Endoscopic treatment of paranasal sinus mucoceles in children
Magnetic Resonance Imaging / Cystic Fibrosis / Endoscopy / Humans / Child / Female / Male / Paranasal Sinuses / Clinical Sciences / X ray Computed Tomography / Endoscopic Sinus Surgery / Female / Male / Paranasal Sinuses / Clinical Sciences / X ray Computed Tomography / Endoscopic Sinus Surgery
Cl Transport in Complemented CF Bronchial Epithelial Cells Correlates with CFTR mRNA Expression Levels
Cystic Fibrosis / Immunohistochemistry / Gene expression / Cell line / Humans / cyclic AMP / Cellular Physiology / Medical Physiology / Gene Dosage / Phenotype / mRna expression levels / Epithelial cells / Bronchial Epithelial Cells / Ion Transport / Transgene Expression / Electric Conductivity / Plasma Membrane / Full Length Movies / Gene Expression Regulation / cyclic AMP / Cellular Physiology / Medical Physiology / Gene Dosage / Phenotype / mRna expression levels / Epithelial cells / Bronchial Epithelial Cells / Ion Transport / Transgene Expression / Electric Conductivity / Plasma Membrane / Full Length Movies / Gene Expression Regulation
Infección bronquial crónica: el problema de Pseudomonas aeruginosa
Biofilms / Cystic Fibrosis / Quality of life / Virology / Ecological Niche Modeling / Humans / Chronic Disease / Antimicrobial resistance / Pseudomonas aeruginosa / Clinical Sciences / Anti-Bacterial Agents / Chronic obstructive pulmonary disease / Bronchiectasis / Pseudomonas Aeruginosa / Pulmonary Function / Haemophilus influenzae / Humans / Chronic Disease / Antimicrobial resistance / Pseudomonas aeruginosa / Clinical Sciences / Anti-Bacterial Agents / Chronic obstructive pulmonary disease / Bronchiectasis / Pseudomonas Aeruginosa / Pulmonary Function / Haemophilus influenzae
Aislamiento de Nocardia en pacientes con fibrosis quística
Cystic Fibrosis / Arch / Clinical Sciences
Aspergillus fumigatus y Candida albicans en la fibrosis quística: significado clínico e inmunorrespuestas séricas específicas de inmunoglobulinas G, A y M
Cystic Fibrosis / Candida albicans / Aspergillus fumigatus / Clinical Sciences
Consenso español para la prevención y el tratamiento de la infección bronquial por Pseudomonas aeruginosa en el paciente con fibrosis quística
Cystic Fibrosis / Humans / Chronic Disease / Pseudomonas aeruginosa / Anti-Bacterial Agents / Disease Progression / Pseudomonas Aeruginosa / Disease Progression / Pseudomonas Aeruginosa
Tratamiento con azitromicina en la fibrosis quística
Cystic Fibrosis / Medicina Clinica
Tolerabilidad de la inhalación de dos soluciones salinas hipertónicas en pacientes con fibrosis quística
Cystic Fibrosis / Hyaluronic Acid / Medicina Clinica
Seguimento nutricional de pacientes com fibrose cística: papel do aconselhamento nutricional
Cystic Fibrosis / Adolescent / Malnutrition / Humans / Child / Female / Male / Infant / Dietary Supplements / Nutritional Status / Nutrition Education / Energy Intake / Female / Male / Infant / Dietary Supplements / Nutritional Status / Nutrition Education / Energy Intake
Application of Fetal DNA Detection in Maternal Plasma: A Prenatal Diagnosis Unit Experience
Cystic Fibrosis / Fluorescence / DNA / real time PCR / Pregnancy / Humans / Mutation / Case Study / Female / Polymerase Chain Reaction / DNA sequence design / Prenatal Diagnosis / Huntington disease / Fetus / Clinical Application / Humans / Mutation / Case Study / Female / Polymerase Chain Reaction / DNA sequence design / Prenatal Diagnosis / Huntington disease / Fetus / Clinical Application
Candida dubliniensis bloodstream infection: a fatal case in a lung transplant recipient
Cystic Fibrosis / Humans / Candida / Male / Candidiasis / Clinical Sciences / Adult / Heart and Lung Transplantation / Clinical Sciences / Adult / Heart and Lung Transplantation
Mediastinal Mass Due to Aspergillus fumigatus After Lung Transplantation: A Case Report
Magnetic Resonance Imaging / Cystic Fibrosis / Case Report / Humans / Female / Cyclic peptides / Aspergillus fumigatus / Recurrence / Anti-Bacterial Agents / Adult / Immunocompromised host / Voriconazole / Antifungal Agents / Combination drug therapy / Triazoles / Heart and Lung Transplantation / Aspergillosis / Thoracoscopy / Cyclic peptides / Aspergillus fumigatus / Recurrence / Anti-Bacterial Agents / Adult / Immunocompromised host / Voriconazole / Antifungal Agents / Combination drug therapy / Triazoles / Heart and Lung Transplantation / Aspergillosis / Thoracoscopy
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