Cystic Fibrosis

Exopolysaccharides produced by Burkholderia cenocepacia recA lineages IIIA and IIIB

Mass Spectrometry / Cystic Fibrosis / NMR Spectroscopy / Magnetic Resonance Spectroscopy / Humans / Gas Chromatography / Clinical Sciences / Burkholderia Cepacia / Gas Chromatography / Clinical Sciences / Burkholderia Cepacia

Burkholderia cepacia complex species: health hazards and biotechnological potential

Microbiology / Cystic Fibrosis / Medical Microbiology / Phylogeny / Humans / Burkholderia Cepacia Complex

SMAP-29: a potent antibacterial and antifungal peptide from sheep leukocytes

Kinetics / Cystic Fibrosis / Scanning Electron Microscopy / Antibiotic Resistance / Humans / Circular Dichroism / Escherichia coli / Sheep / Cryptococcus Neoformans / Animals / Antimicrobial activity / Staphylococcus aureus / Drug Design / Peptides / Proteins / Pseudomonas aeruginosa / Anti-Bacterial Agents / Protein Secondary Structure Prediction / Antifungal Agents / Pseudomonas Aeruginosa / Protein Conformation / Leukocytes / Methicillin Resistant Staphylococcus Aureus / Blood Proteins / Biochemistry and cell biology / Minimum inhibitory concentration / Hemolysis / Circular Dichroism / Escherichia coli / Sheep / Cryptococcus Neoformans / Animals / Antimicrobial activity / Staphylococcus aureus / Drug Design / Peptides / Proteins / Pseudomonas aeruginosa / Anti-Bacterial Agents / Protein Secondary Structure Prediction / Antifungal Agents / Pseudomonas Aeruginosa / Protein Conformation / Leukocytes / Methicillin Resistant Staphylococcus Aureus / Blood Proteins / Biochemistry and cell biology / Minimum inhibitory concentration / Hemolysis

Structural Elucidation of a Novel B. cenocepacia ET-12 Lipooligosaccharide Isolated from a Cystic Fibrosis Patient after Lung Transplantation

Organic Chemistry / Immunology / Cystic Fibrosis / Innate immunity / Structural Analysis / Bacteria / Organic / Structure Elucidation / Reaction Mechanism / Heart and Lung Transplantation / Bacteria / Organic / Structure Elucidation / Reaction Mechanism / Heart and Lung Transplantation

Endosomal hyperacidification in cystic fibrosis is due to defective nitric oxide-cylic GMP signalling cascade

Cystic Fibrosis / Signal Transduction / Humans / Nitric oxide / Pseudomonas aeruginosa / Phosphodiesterase Inhibitors / Sodium channel / Pseudomonas Aeruginosa / Hydrogen-Ion Concentration / Endosomes / Guanylate Cyclase / cyclic GMP / Biochemistry and cell biology / Phosphodiesterase Inhibitors / Sodium channel / Pseudomonas Aeruginosa / Hydrogen-Ion Concentration / Endosomes / Guanylate Cyclase / cyclic GMP / Biochemistry and cell biology

Ecto-ADP-ribosyltransferase activity of Pseudomonas aeruginosa exoenzyme S

Cystic Fibrosis / Biological Sciences / Infection and immunity / Humans / Tissue culture / Bacterial Toxins / Animals / Animal Model / Pseudomonas aeruginosa / apolipoprotein A-I / Amino Acid Profile / Molecular Mass / Virulence factor / Pseudomonas Aeruginosa / Molecular weight / Rabbits / Structure Function / Catalytic Activity / Glutamic Acid / Pleura / Immunoglobulin / Low molecular weight / Blood Proteins / immunoglobulin G / Blood Plasma / Bacterial Toxins / Animals / Animal Model / Pseudomonas aeruginosa / apolipoprotein A-I / Amino Acid Profile / Molecular Mass / Virulence factor / Pseudomonas Aeruginosa / Molecular weight / Rabbits / Structure Function / Catalytic Activity / Glutamic Acid / Pleura / Immunoglobulin / Low molecular weight / Blood Proteins / immunoglobulin G / Blood Plasma

Optimal Design for Model Discrimination and Parameter Estimation for Itraconazole Population Pharmacokinetics in Cystic Fibrosis Patients

Cystic Fibrosis / Allergic bronchopulmonary aspergillosis / Parameter estimation / Humans / Data Collection / Antifungal Agents / Itraconazole / Optimal Design / Capsules / Structural model / Antifungal Agents / Itraconazole / Optimal Design / Capsules / Structural model

Cl Transport in Complemented CF Bronchial Epithelial Cells Correlates with CFTR mRNA Expression Levels

Cystic Fibrosis / Immunohistochemistry / Gene expression / Cell line / Humans / cyclic AMP / Cellular Physiology / Medical Physiology / Gene Dosage / Phenotype / mRna expression levels / Epithelial cells / Bronchial Epithelial Cells / Ion Transport / Transgene Expression / Electric Conductivity / Plasma Membrane / Full Length Movies / Gene Expression Regulation / Chlorides / cyclic AMP / Cellular Physiology / Medical Physiology / Gene Dosage / Phenotype / mRna expression levels / Epithelial cells / Bronchial Epithelial Cells / Ion Transport / Transgene Expression / Electric Conductivity / Plasma Membrane / Full Length Movies / Gene Expression Regulation / Chlorides

Sponge-associated microbial Antarctic communities exhibiting antimicrobial activity against Burkholderia cepacia complex bacteria

Engineering / Technology / Principal Component Analysis / Biotechnology / Cystic Fibrosis / Porifera / Biological Sciences / Phylogeny / Humans / Design studies / Volatile Organic Compounds / Animals / Antimicrobial activity / Polymerase Chain Reaction / Phylogenetic analysis / VOC / Anti-Bacterial Agents / Drug Stability / Burkholderia Cepacia Complex / Whole Body / Pathogenic Bacteria / Microbial community / Random amplified polymorphic DNA / Pseudoalteromonas / Porifera / Biological Sciences / Phylogeny / Humans / Design studies / Volatile Organic Compounds / Animals / Antimicrobial activity / Polymerase Chain Reaction / Phylogenetic analysis / VOC / Anti-Bacterial Agents / Drug Stability / Burkholderia Cepacia Complex / Whole Body / Pathogenic Bacteria / Microbial community / Random amplified polymorphic DNA / Pseudoalteromonas

Phosphonic pseudopeptides as human neutrophil elastase inhibitors—a combinatorial approach

Organic Chemistry / Cystic Fibrosis / Rheumatoid Arthritis / Single molecule / Humans / Trypsin / Serine Proteases / Second Order / Gingiva / Bioorganic and medicinal Chemistry / Cell Proliferation / Biological activity / Human Fibroblasts / Serine Protease / Cell Survival / Tumor Growth / Molecular Structure / Chymotrypsin / Trypsin / Serine Proteases / Second Order / Gingiva / Bioorganic and medicinal Chemistry / Cell Proliferation / Biological activity / Human Fibroblasts / Serine Protease / Cell Survival / Tumor Growth / Molecular Structure / Chymotrypsin

SMAP-29: a potent antibacterial and antifungal peptide from sheep leukocytes

Kinetics / Cystic Fibrosis / Scanning Electron Microscopy / Antibiotic Resistance / Humans / Circular Dichroism / Escherichia coli / Sheep / Cryptococcus Neoformans / Animals / Antimicrobial activity / Staphylococcus aureus / Drug Design / Peptides / Proteins / Pseudomonas aeruginosa / Anti-Bacterial Agents / Protein Secondary Structure Prediction / Antifungal Agents / Pseudomonas Aeruginosa / Protein Conformation / Leukocytes / Methicillin Resistant Staphylococcus Aureus / Blood Proteins / Biochemistry and cell biology / Minimum inhibitory concentration / Hemolysis / Circular Dichroism / Escherichia coli / Sheep / Cryptococcus Neoformans / Animals / Antimicrobial activity / Staphylococcus aureus / Drug Design / Peptides / Proteins / Pseudomonas aeruginosa / Anti-Bacterial Agents / Protein Secondary Structure Prediction / Antifungal Agents / Pseudomonas Aeruginosa / Protein Conformation / Leukocytes / Methicillin Resistant Staphylococcus Aureus / Blood Proteins / Biochemistry and cell biology / Minimum inhibitory concentration / Hemolysis

Sponge-associated microbial Antarctic communities exhibiting antimicrobial activity against Burkholderia cepacia complex bacteria

Engineering / Technology / Principal Component Analysis / Biotechnology / Cystic Fibrosis / Porifera / Biological Sciences / Phylogeny / Humans / Design studies / Volatile Organic Compounds / Animals / Antimicrobial activity / Polymerase Chain Reaction / Phylogenetic analysis / Anti-Bacterial Agents / Drug Stability / Burkholderia Cepacia Complex / Whole Body / Pathogenic Bacteria / Microbial community / Random amplified polymorphic DNA / Porifera / Biological Sciences / Phylogeny / Humans / Design studies / Volatile Organic Compounds / Animals / Antimicrobial activity / Polymerase Chain Reaction / Phylogenetic analysis / Anti-Bacterial Agents / Drug Stability / Burkholderia Cepacia Complex / Whole Body / Pathogenic Bacteria / Microbial community / Random amplified polymorphic DNA

Is Hydrogen Cyanide a Marker of Burkholderia cepacia Complex?

Mass Spectrometry / Cystic Fibrosis / Clinical Microbiology / Biological Sciences / Humans / Female / Male / Adult / Biological markers / Burkholderia Cepacia Complex / Female / Male / Adult / Biological markers / Burkholderia Cepacia Complex

Transient exocrine pancreatic insufficiency as a possible complication of an enterovirus infection

Cystic Fibrosis / Pancreatitis / Diarrhea / Humans / Child / Male / Differential Diagnosis / Acute Pancreatitis / Chronic Pancreatitis / Public health systems and services research / Viral Infection / Exocrine Pancreatic Insufficiency / Male / Differential Diagnosis / Acute Pancreatitis / Chronic Pancreatitis / Public health systems and services research / Viral Infection / Exocrine Pancreatic Insufficiency

Survival of Burkholderia cepacia on environmental surfaces

Environmental microbiology / Cystic Fibrosis / Hospital Infection / Humans / Stainless Steel / Clinical Sciences / Analysis of Variance / Time Factors / Sputum / Burkholderia Cepacia / Survival Time / Serotyping / Clinical Sciences / Analysis of Variance / Time Factors / Sputum / Burkholderia Cepacia / Survival Time / Serotyping
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