Enzyme activity

A Structural Model of Transcription Elongation

Science / RNA polymerase / Gene expression / Multidisciplinary / Macromolecular X-Ray Crystallography / Transcription / DNA / Mutation / Nucleic acid hybridization / Bacteria / DNA hybridization / Mechanism / Elongation / Enzyme activity / Protein Conformation / Crystalline Structure / Nucleic Acid Conformation / Structural model / Nucleic Acid / single stranded DNA / Functional Properties / Transcription / DNA / Mutation / Nucleic acid hybridization / Bacteria / DNA hybridization / Mechanism / Elongation / Enzyme activity / Protein Conformation / Crystalline Structure / Nucleic Acid Conformation / Structural model / Nucleic Acid / single stranded DNA / Functional Properties

Succinyl-CoA Ligase Deficiency: A Mitochondrial Hepatoencephalomyopathy

Endocrinology / Genetics / Functional Analysis / Cardiology / Hematology / Nephrology / Neurology / Oncology / Pediatrics / Pulmonology / Rheumatology / Epidemiology / Immunology / Nutrition / Magnetic Resonance Imaging / Mitochondria / Public Health / Liver diseases / Brain / Allergy / Mitochondrial DNA / Humans / Sensorineural Hearing Loss / Mutation / Female / Infant / Pediatric / Respiratory Failure / Newborn Infant / Mitochondrial Diseases / Deficiency / Enzyme activity / Amino Acid Profile / Fetus / Liver Failure / Amino Acid Sequence / Base Sequence / Deficit / Laboratory Tests / Glutamic Acid / Translation initiation / Organic Acid / Molecular Sequence Data / DNA mutational analysis / Nephrology / Neurology / Oncology / Pediatrics / Pulmonology / Rheumatology / Epidemiology / Immunology / Nutrition / Magnetic Resonance Imaging / Mitochondria / Public Health / Liver diseases / Brain / Allergy / Mitochondrial DNA / Humans / Sensorineural Hearing Loss / Mutation / Female / Infant / Pediatric / Respiratory Failure / Newborn Infant / Mitochondrial Diseases / Deficiency / Enzyme activity / Amino Acid Profile / Fetus / Liver Failure / Amino Acid Sequence / Base Sequence / Deficit / Laboratory Tests / Glutamic Acid / Translation initiation / Organic Acid / Molecular Sequence Data / DNA mutational analysis

Succinyl-CoA Ligase Deficiency: A Mitochondrial Hepatoencephalomyopathy

Endocrinology / Genetics / Functional Analysis / Cardiology / Hematology / Nephrology / Neurology / Oncology / Pediatrics / Pulmonology / Rheumatology / Epidemiology / Immunology / Nutrition / Magnetic Resonance Imaging / Mitochondria / Public Health / Liver diseases / Brain / Allergy / Mitochondrial DNA / Humans / Sensorineural Hearing Loss / Mutation / Female / Infant / Pediatric / Respiratory Failure / Newborn Infant / Mitochondrial Diseases / Deficiency / Enzyme activity / Amino Acid Profile / Fetus / Liver Failure / Amino Acid Sequence / Base Sequence / Deficit / Laboratory Tests / Glutamic Acid / Translation initiation / Organic Acid / Molecular Sequence Data / DNA mutational analysis / Nephrology / Neurology / Oncology / Pediatrics / Pulmonology / Rheumatology / Epidemiology / Immunology / Nutrition / Magnetic Resonance Imaging / Mitochondria / Public Health / Liver diseases / Brain / Allergy / Mitochondrial DNA / Humans / Sensorineural Hearing Loss / Mutation / Female / Infant / Pediatric / Respiratory Failure / Newborn Infant / Mitochondrial Diseases / Deficiency / Enzyme activity / Amino Acid Profile / Fetus / Liver Failure / Amino Acid Sequence / Base Sequence / Deficit / Laboratory Tests / Glutamic Acid / Translation initiation / Organic Acid / Molecular Sequence Data / DNA mutational analysis

No carnitine palmitoyltransferase deficiency in skeletal muscle in 18 malignant hyperthermia susceptible individuals

Skeletal muscle biology / Adolescent / Humans / Female / Male / Medical Physiology / Enzyme / Clinical Sciences / Skeletal Muscle / Adult / Neuromuscular Disorders / Fatty Acid / Enzyme activity / Malignant Hyperthermia / Neurosciences / Medical Physiology / Enzyme / Clinical Sciences / Skeletal Muscle / Adult / Neuromuscular Disorders / Fatty Acid / Enzyme activity / Malignant Hyperthermia / Neurosciences

Human dehydroepiandrosterone sulfotransferase pharmacogenetics: quantitative Western analysis and gene sequence polymorphisms

Polymorphism / Western blotting / Humans / Liver / Animals / Polymerase Chain Reaction / Enzyme / DNA isolation / Genetic Polymorphism / Dehydroepiandrosterone / Enzyme activity / Amino Acid Profile / Amino Acid Sequence / Recombinant Proteins / Enzymatic Activity / Allele Frequency / Nucleotides / Biochemistry and cell biology / Transient Expression / Polymerase Chain Reaction / Enzyme / DNA isolation / Genetic Polymorphism / Dehydroepiandrosterone / Enzyme activity / Amino Acid Profile / Amino Acid Sequence / Recombinant Proteins / Enzymatic Activity / Allele Frequency / Nucleotides / Biochemistry and cell biology / Transient Expression

Transport deficient (TR−) hyperbilirubinemic rats are resistant to acetaminophen hepatotoxicity

Drug metabolism / Liver / Animals / Male / Glutathione / Biochemical / Enzyme / MRP / mRna expression levels / Npsh / Rats / PBS / Wistar Rats / Enzyme activity / BIOCHEMICAL PHARMACOLOGY / Acetaminophen / Hyperbilirubinemia / Biochemical / Enzyme / MRP / mRna expression levels / Npsh / Rats / PBS / Wistar Rats / Enzyme activity / BIOCHEMICAL PHARMACOLOGY / Acetaminophen / Hyperbilirubinemia

Human Mitochondrial Manganese Superoxide Dismutase Polymorphic Variant Ile58Thr Reduces Activity by Destabilizing the Tetrameric Interface † , ‡

Biochemistry / Polymorphism / Electrochemistry / Oxidative Stress / Amyotrophic Lateral Sclerosis / Free Radical / Crystal structure / Humans / Temperature / Superoxide Dismutase / Phenotype / Enzyme / Body Temperature / Temperature Dependence / Active site / Thermal Stability / Oxidative Damage / Genetic variation / Enzyme activity / Protein Conformation / Elevated Temperature / Site-directed Mutagenesis / Nervous System Diseases / Biochemistry and cell biology / Molecular Structure / Melting Temperature / Molecular Sequence Data / Free Radical / Crystal structure / Humans / Temperature / Superoxide Dismutase / Phenotype / Enzyme / Body Temperature / Temperature Dependence / Active site / Thermal Stability / Oxidative Damage / Genetic variation / Enzyme activity / Protein Conformation / Elevated Temperature / Site-directed Mutagenesis / Nervous System Diseases / Biochemistry and cell biology / Molecular Structure / Melting Temperature / Molecular Sequence Data

Evaluación de la posible adulteración de mieles de abeja comerciales de origen costarricense al compararlas con mieles artesanales provenientes de apiarios específicos

Nutrition and Dietetics / Apis mellifera / HPLC / Quality Standard / Enzyme activity / Indexation / Food Products / Indexation / Food Products

Mitochondrial gene expression and respiratory enzyme activities in cardiac diseases

Mitochondria / Gene expression / Biological Sciences / Mitochondrial DNA / Humans / Aortic stenosis / Female / Male / Physical sciences / Cytochrome c oxidase / Enzyme / Steady state / Clinical Sciences / Middle Aged / Oxidative phosphorylation / Multienzyme complexes / Enzyme activity / Pressure Gradient / Cardiac Disease / Biochemistry and cell biology / Heart Diseases / Aortic stenosis / Female / Male / Physical sciences / Cytochrome c oxidase / Enzyme / Steady state / Clinical Sciences / Middle Aged / Oxidative phosphorylation / Multienzyme complexes / Enzyme activity / Pressure Gradient / Cardiac Disease / Biochemistry and cell biology / Heart Diseases

Carnitine palmitoyltransferase I, carnitine palmitoyltransferase II, and Acyl-CoA oxidase activities in atlantic salmon (Salmo salar)

Engineering / Skeletal muscle biology / Lipids / Liver / Fatty acids / Animals / Oxidoreductases / Fatty Acid Oxidation / Temperature / Atlantic Salmon / Enzyme / Myocardium / Isoenzymes / Salmo salar / Fatty Acid / Enzyme activity / Oxidation-Reduction / Muscle Activity / High energy / Animals / Oxidoreductases / Fatty Acid Oxidation / Temperature / Atlantic Salmon / Enzyme / Myocardium / Isoenzymes / Salmo salar / Fatty Acid / Enzyme activity / Oxidation-Reduction / Muscle Activity / High energy

Sweet cassava polysaccharide extracts protects against CCl4 liver injury in Wistar rats

real time PCR / Enzyme / Manihot esculenta / Antioxidant Activity / Antioxidant enzyme / Rat / Food Sciences / Enzyme activity / Extract / Food Hydrocolloids / Rat / Food Sciences / Enzyme activity / Extract / Food Hydrocolloids

Introducing a novel human mtDNA mutation into the Paracoccus denitrificans COX I gene explains functional deficits in a patient

Genetics / Cognitive Science / Neurogenetics / Mitochondrial DNA / Humans / Models / Mutation / Female / Animals / Bacteria / Cytochrome c oxidase / Gene / Phenotype / Mitochondrial Genome / Enzyme / Gen / Adult / Enzyme activity / Protein Conformation / Neurosciences / DNA mutational analysis / Models / Mutation / Female / Animals / Bacteria / Cytochrome c oxidase / Gene / Phenotype / Mitochondrial Genome / Enzyme / Gen / Adult / Enzyme activity / Protein Conformation / Neurosciences / DNA mutational analysis

Postischemic hyperoxia reduces hippocampal pyruvate dehydrogenase activity

Free Radicals / Mitochondria / Energy Metabolism / Western blotting / Free Radical / Dogs / Hippocampus / Cardiac arrest / Anoxia / Female / Animals / Enzyme / High Pressure Liquid Chromatography / Oxidative stress and free radical biology and medicine / Cerebral Ischemia / Enzyme activity / Enzyme Linked Immunosorbent Assay / Ventricular Fibrillation / Biochemistry and cell biology / Myocardial Ischemia / Dogs / Hippocampus / Cardiac arrest / Anoxia / Female / Animals / Enzyme / High Pressure Liquid Chromatography / Oxidative stress and free radical biology and medicine / Cerebral Ischemia / Enzyme activity / Enzyme Linked Immunosorbent Assay / Ventricular Fibrillation / Biochemistry and cell biology / Myocardial Ischemia

Resistance to a Protein Farnesyltransferase Inhibitor in Plasmodium falciparum

Malaria / Biological Chemistry / Biological Sciences / Protein-Protein Interaction / Humans / Sequence alignment / Animals / Drug Resistance / Biological / Chemical Analysis / CHEMICAL SCIENCES / Plasmodium falciparum / Enzyme activity / Protozoan Proteins / Imidazoles / Amino Acid Sequence / Quinolines / Binding Site / Molecular Structure / Molecular Sequence Data / Sequence alignment / Animals / Drug Resistance / Biological / Chemical Analysis / CHEMICAL SCIENCES / Plasmodium falciparum / Enzyme activity / Protozoan Proteins / Imidazoles / Amino Acid Sequence / Quinolines / Binding Site / Molecular Structure / Molecular Sequence Data

Ornithine carbamoyltransferase deficiency. A new variant with subnormal enzyme activity

Kinetics / Humans / Liver / Male / Temperature / Infant / Clinical Sciences / Amino Acids / Enzyme activity / Hydrogen-Ion Concentration / Infant / Clinical Sciences / Amino Acids / Enzyme activity / Hydrogen-Ion Concentration
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