Enzyme activity

Pharmacological interference with intestinal bile acid transport reduces plasma cholesterol in LDL receptor/apoE deficiency

Physiology / Mice / Cholesterol / Female / Animals / Medical Physiology / LDL-cholesterol / Enzyme / Coronary heart disease / Enzyme activity / Familial Hypercholesterolemia / ADJUVANT THERAPY / Biochemistry and cell biology / Gene Expression Regulation / Medical Physiology / LDL-cholesterol / Enzyme / Coronary heart disease / Enzyme activity / Familial Hypercholesterolemia / ADJUVANT THERAPY / Biochemistry and cell biology / Gene Expression Regulation

Galactosialidosis: A direct evidence that a 46-kilodalton protein restores deficient enzyme activities in fibroblasts

Humans / Inborn errors of metabolism / Proteins / Neuraminidase / Enzyme activity / Molecular weight / Human Fibroblasts / Biochemistry and cell biology / Molecular weight / Human Fibroblasts / Biochemistry and cell biology

Ser72Pro active-site disease mutation in human lysosomal aspartylglucosaminidase: abnormal intracellular processing and evidence for extracellular activation

Biological Sciences / Cercopithecus aethiops / Humans / Animals / Human Molecular Genetics / Endoplasmic Reticulum / Proline / Enzyme / Active site / Enzyme activity / Amino Acid Profile / Lysosomes / Lysosomal Storage Diseases / Transient Expression / Proteolytic activity / Endoplasmic Reticulum / Proline / Enzyme / Active site / Enzyme activity / Amino Acid Profile / Lysosomes / Lysosomal Storage Diseases / Transient Expression / Proteolytic activity

Oxidative DNA damage in vitamin C-supplemented guinea pigs after intratracheal instillation of diesel exhaust particles

Oxidative Stress / DNA damage / DNA / Toxicity / vitamin C / Vehicle Emissions / Female / Animals / Male / Glutathione Peroxidase / Superoxide Dismutase / Dep / Antioxidant enzyme / Diesel Fuel / Particle / Ascorbic Acid / Trachea / Oxidative Damage / Guinea Pig / Particulate Matter / Enzyme activity / Amino Acid Profile / Oxidative Dna Damage / Health Effect / Glutathione Reductase / Protein Oxidation / Vehicle Emissions / Female / Animals / Male / Glutathione Peroxidase / Superoxide Dismutase / Dep / Antioxidant enzyme / Diesel Fuel / Particle / Ascorbic Acid / Trachea / Oxidative Damage / Guinea Pig / Particulate Matter / Enzyme activity / Amino Acid Profile / Oxidative Dna Damage / Health Effect / Glutathione Reductase / Protein Oxidation

Purification and Characterization of an a-Glucosidase from Rhizobium sp. (Robinia pseudoacacia L.) Strain USDA 4280

Kinetics / Enzyme / Enzyme activity / Gel electrophoresis / Polyacrylamide Gel Electrophoresis / Cation Exchange / Ammonium Sulfate / Cation Exchange / Ammonium Sulfate

Characteristics of Trametes villosa laccase adsorbed on aluminum hydroxide

Environmental Biotechnology / Oxygen Uptake / Soil Remediation / Humic acid / Enzyme / Infrared / Secondary Structure / IR Spectroscopy / Enzyme activity / Adsorption Isotherm Models / Microbial enzyme Technology / Short Range Order / Kinetic Parameter / Infrared / Secondary Structure / IR Spectroscopy / Enzyme activity / Adsorption Isotherm Models / Microbial enzyme Technology / Short Range Order / Kinetic Parameter

Potential control of horseradish peroxidase immobilization on gold electrode

Self Assembly / Enzyme / CHEMICAL SCIENCES / Enzyme activity / Atomic Force Microscope / X Ray Photoelectron Spectroscopy / Modified Electrode / X Ray Photoelectron Spectroscopy / Modified Electrode

Antioxidant erythrocyte enzyme activities during oral contraception

Contraception / Adolescent / Antioxidants / Humans / Pyruvate Kinase / Female / Catalase / Glutathione Peroxidase / Superoxide Dismutase / Clinical Sciences / Adult / Public health systems and services research / Enzyme activity / Erythrocytes / Oral Contraceptive / Female / Catalase / Glutathione Peroxidase / Superoxide Dismutase / Clinical Sciences / Adult / Public health systems and services research / Enzyme activity / Erythrocytes / Oral Contraceptive

Ritmo circadiano de la actividad enzimática digestiva del camarón blanco Litopenaeus vannamei y su efecto en el horario de alimentación

Manejo De Recursos Naturales / Circadian Rhythm / Litopenaeus Vannamei / Enzyme activity / Enzymatic Activity

Human Mitochondrial Manganese Superoxide Dismutase Polymorphic Variant Ile58Thr Reduces Activity by Destabilizing the Tetrameric Interface † , ‡

Biochemistry / Polymorphism / Electrochemistry / Oxidative Stress / Amyotrophic Lateral Sclerosis / Free Radical / Crystal structure / Humans / Temperature / Superoxide Dismutase / Phenotype / Enzyme / Body Temperature / Temperature Dependence / Active site / Thermal Stability / Oxidative Damage / Genetic variation / Enzyme activity / Protein Conformation / Elevated Temperature / Site-directed Mutagenesis / Nervous System Diseases / Biochemistry and cell biology / Molecular Structure / Melting Temperature / Molecular Sequence Data / Free Radical / Crystal structure / Humans / Temperature / Superoxide Dismutase / Phenotype / Enzyme / Body Temperature / Temperature Dependence / Active site / Thermal Stability / Oxidative Damage / Genetic variation / Enzyme activity / Protein Conformation / Elevated Temperature / Site-directed Mutagenesis / Nervous System Diseases / Biochemistry and cell biology / Molecular Structure / Melting Temperature / Molecular Sequence Data

Mouse Model for Human Arginase Deficiency

Cellular Biology / Gene Therapy / Biological Sciences / Molecular and cellular biology / Humans / Kidney / Liver / Mice / Female / Animals / Male / Nitrogen / Detoxification / Enzyme / Human Genome / Mouse Model / Mammary gland / Enzyme activity / Homologous Recombination / Quaternary Ammonium Compounds / Knockout Mice / Glutamic Acid / Growth Retardation / Kidney / Liver / Mice / Female / Animals / Male / Nitrogen / Detoxification / Enzyme / Human Genome / Mouse Model / Mammary gland / Enzyme activity / Homologous Recombination / Quaternary Ammonium Compounds / Knockout Mice / Glutamic Acid / Growth Retardation

Genomic identification and biochemical characterization of a second spermidine/spermine N 1-acetyltransferase

Biological Sciences / Cell line / Humans / Expressed Sequence Tags / Biochemical / Human Brain / Enzyme / High Pressure Liquid Chromatography / CHEMICAL SCIENCES / Human Genome / Substrate Specificity / Enzyme activity / Amino Acid Profile / Genome sequence / Amino Acid Sequence / Molecular Sequence Data / Human Brain / Enzyme / High Pressure Liquid Chromatography / CHEMICAL SCIENCES / Human Genome / Substrate Specificity / Enzyme activity / Amino Acid Profile / Genome sequence / Amino Acid Sequence / Molecular Sequence Data

3-Hydroxy-3-methylglutaryl-coenzyme A (HMG-CoA) lyase deficiency in Saudi Arabia

Magnetic Resonance Imaging / Saudi Arabia / Brain / Humans / Female / Male / Magnetic Resonance / Early development / Enzyme / Clinical Sciences / Newborn Infant / Atrophy / Consanguinity / Computerized tomography / Enzyme activity / Lymphocytes / Human Fibroblasts / X ray Computed Tomography / Clinical Presentation / White Matter Lesions / Organic Acid / Mass Spectrometer / Male / Magnetic Resonance / Early development / Enzyme / Clinical Sciences / Newborn Infant / Atrophy / Consanguinity / Computerized tomography / Enzyme activity / Lymphocytes / Human Fibroblasts / X ray Computed Tomography / Clinical Presentation / White Matter Lesions / Organic Acid / Mass Spectrometer

Enzyme activity in cryobiological systems

Cryobiology / Medical Physiology / Enzyme activity / Biochemistry and cell biology

Mitochondrial activity in pompe’s disease

Electron Microscopy / Mitochondria / Pediatric Neurology / Biopsy / Humans / Female / Muscles / Infant / Mitochondrial Respiratory Chain / Differential Diagnosis / Electron Transport / Enzyme / Newborn Infant / Skeletal Muscle / Specific Activity / Enzyme activity / Glycogen / Neurosciences / Oxidation-Reduction / Citrate Synthase / Clinical Diagnosis / Oxidative Metabolism / Female / Muscles / Infant / Mitochondrial Respiratory Chain / Differential Diagnosis / Electron Transport / Enzyme / Newborn Infant / Skeletal Muscle / Specific Activity / Enzyme activity / Glycogen / Neurosciences / Oxidation-Reduction / Citrate Synthase / Clinical Diagnosis / Oxidative Metabolism

Equine biochemical multiple acyl-CoA dehydrogenase deficiency (MADD) as a cause of rhabdomyolysis

Molecular Genetics / Female / Animals / Male / Horses / Enzyme / Clinical Sciences / Enzyme activity / Metabolic Disorder / Clinical Signs / Lactic Acid / Rhabdomyolysis / Organic Acid / Enzyme / Clinical Sciences / Enzyme activity / Metabolic Disorder / Clinical Signs / Lactic Acid / Rhabdomyolysis / Organic Acid
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