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Oxidative phosphorylation
Oxidative phosphorylation
AIF deficiency compromises oxidative phosphorylation
Membrane Proteins / Mitochondria / Apoptosis / Biological Sciences / Phylogeny / Brain / Humans / Glucose / Mice / Animals / Retina / Retinal Degeneration / Mitochondrial Respiratory Chain / Programmed cell death / Myocardium / Oxidative phosphorylation / Yeasts / Homologous Recombination / Lactic Acid / Adenosine Triphosphate / Brain / Humans / Glucose / Mice / Animals / Retina / Retinal Degeneration / Mitochondrial Respiratory Chain / Programmed cell death / Myocardium / Oxidative phosphorylation / Yeasts / Homologous Recombination / Lactic Acid / Adenosine Triphosphate
ATP-Dependent Lon Protease Controls Tumor Bioenergetics by Reprogramming Mitochondrial Activity
Mitochondria / Humans / Mice / Melanoma / Animals / Haploinsufficiency / Oxidative phosphorylation / Cell Proliferation / Skin Neoplasms / Haploinsufficiency / Oxidative phosphorylation / Cell Proliferation / Skin Neoplasms
Nitric oxide increases oxidative phosphorylation efficiency
Bioenergetics / Nitric oxide / Animals / Rats / Oxidative phosphorylation / Succinic Acid / Oxygen Consumption / Glutamic Acid / Biochemistry and cell biology / Succinic Acid / Oxygen Consumption / Glutamic Acid / Biochemistry and cell biology
Conversion of biomembrane-produced energy into electric form. I. Submitochondrial particles
Electron Microscopy / Metabolism / Membranes / Kinetics / Calcium / Mitochondria / Fluorescent Dyes and Reagents / Vibration / Biological Sciences / Permeability / Mercury / Animals / Physical sciences / Light / Plants / Potassium / Absorption / Electron Transport / Cattle / Anti-Bacterial Agents / Ascorbic Acid / Rats / Oxygen / Myocardium / Oxidative phosphorylation / Spectrum analysis / Phosphates / Energy Transfer / Cytochromes / Rabbits / Quinolines / NAD / Cyanides / Quaternary Ammonium Compounds / Organometallic Compounds / Hydrogen-Ion Concentration / Oxygen Consumption / Boron Compounds / Ions / Micrococcus luteus / Photophosphorylation / Biochemistry and cell biology / aniline Compounds / Adenosine Triphosphate / Chloroplasts / Mitochondria / Fluorescent Dyes and Reagents / Vibration / Biological Sciences / Permeability / Mercury / Animals / Physical sciences / Light / Plants / Potassium / Absorption / Electron Transport / Cattle / Anti-Bacterial Agents / Ascorbic Acid / Rats / Oxygen / Myocardium / Oxidative phosphorylation / Spectrum analysis / Phosphates / Energy Transfer / Cytochromes / Rabbits / Quinolines / NAD / Cyanides / Quaternary Ammonium Compounds / Organometallic Compounds / Hydrogen-Ion Concentration / Oxygen Consumption / Boron Compounds / Ions / Micrococcus luteus / Photophosphorylation / Biochemistry and cell biology / aniline Compounds / Adenosine Triphosphate / Chloroplasts
ATP-Dependent Lon Protease Controls Tumor Bioenergetics by Reprogramming Mitochondrial Activity
Mitochondria / Humans / Mice / Melanoma / Animals / Haploinsufficiency / Oxidative phosphorylation / Cell Proliferation / Skin Neoplasms / Haploinsufficiency / Oxidative phosphorylation / Cell Proliferation / Skin Neoplasms
Cell Biological Consequences of Mitochondrial NADH: Ubiquinone Oxidoreductase Deficiency
Cell Biology / Mitochondria / Mitochondrial DNA / Humans / Animals / Inborn errors of metabolism / Cells / Skeletal Muscle / Current / Oxidative phosphorylation / Inborn errors of metabolism / Cells / Skeletal Muscle / Current / Oxidative phosphorylation
Perilipin 2 Improves Insulin Sensitivity in Skeletal Muscle Despite Elevated Intramuscular Lipid Levels
Skeletal muscle biology / Diabetes / Membrane Proteins / RNA interference / Insulin Resistance / Cell line / Mice / Electroporation / Female / Animals / Gene transfer techniques / Male / Lipid metabolism / Rats / Oxidative phosphorylation / Wistar Rats / Recombinant Proteins / Gene expression profiling / Cell line / Mice / Electroporation / Female / Animals / Gene transfer techniques / Male / Lipid metabolism / Rats / Oxidative phosphorylation / Wistar Rats / Recombinant Proteins / Gene expression profiling
Quantification of muscle mitochondrial oxidative phosphorylation enzymesvia histochemical staining of blue native polyacrylamide gels
Chemical Engineering / Analytical Chemistry / Skeletal muscle biology / Mitochondria / Humans / Animals / Muscles / Sodium Dodecyl Sulfate-Polyacrylamide Gel Electrophoresis / Cattle / Electrophoresis / Rats / Oxidative phosphorylation / Detergents / Succinate Dehydrogenase / Biochemistry and cell biology / Animals / Muscles / Sodium Dodecyl Sulfate-Polyacrylamide Gel Electrophoresis / Cattle / Electrophoresis / Rats / Oxidative phosphorylation / Detergents / Succinate Dehydrogenase / Biochemistry and cell biology
Normal Serum Alanine Concentration Differentiates Transient Neonatal Lactic Acidemia from an Inborn Error of Energy Metabolism
Decision Making / Energy Metabolism / Mitochondrial DNA / Humans / Mutation / Inborn errors of metabolism / Differential Diagnosis / Clinical Sciences / Newborn Infant / Mitochondrial dysfunction / Mitochondrial Diseases / Pilot study / Oxidative phosphorylation / Alanine / Pilot Projects / Lactic Acid / Inborn errors of metabolism / Differential Diagnosis / Clinical Sciences / Newborn Infant / Mitochondrial dysfunction / Mitochondrial Diseases / Pilot study / Oxidative phosphorylation / Alanine / Pilot Projects / Lactic Acid
Mitochondrial complex i deficiency in a female with multiplex arthrogryposis congenita
Skeletal muscle biology / Mitochondria / Energy Metabolism / Pediatric Neurology / Biopsy / Humans / Child / Female / Specific Activity / Oxidative phosphorylation / Neurosciences / Arthrogryposis / Humans / Child / Female / Specific Activity / Oxidative phosphorylation / Neurosciences / Arthrogryposis
Mutant Mitochondrial Elongation Factor G1 and Combined Oxidative Phosphorylation Deficiency
Mitochondria / Medicine / Mitochondrial DNA / Humans / Mutation / Microcephaly / Female / Male / Infant / Newborn Infant / Mitochondrial Diseases / New England / Guanosine Triphosphate / Oxidative phosphorylation / Deficiency / Liver Failure / Deficit / New England Journalof Medicine / Protein Biosynthesis / Mitochondrial Proteins / Microcephaly / Female / Male / Infant / Newborn Infant / Mitochondrial Diseases / New England / Guanosine Triphosphate / Oxidative phosphorylation / Deficiency / Liver Failure / Deficit / New England Journalof Medicine / Protein Biosynthesis / Mitochondrial Proteins
Influence of mitochondrial DNA level on cellular energy metabolism: implications for mitochondrial diseases
Bioenergetics / Energy Metabolism / Transcription / Cell line / Mitochondrial DNA / Humans / Computer Simulation / Muscle / Animals / Mitochondrial Respiratory Chain / Expression / Mitochondrial Diseases / Energy Production / Replication / Oxidative phosphorylation / Biochemistry and cell biology / Humans / Computer Simulation / Muscle / Animals / Mitochondrial Respiratory Chain / Expression / Mitochondrial Diseases / Energy Production / Replication / Oxidative phosphorylation / Biochemistry and cell biology
Glutamyl-tRNA Gln amidotransferase is essential for mammalian mitochondrial translation in vivo
Mitochondria / Protein Stability / Biological Sciences / Humans / Reactive Oxygen Species / Mice / Animals / Tandem Mass Spectrometry / Biochemical / Phenotype / CHEMICAL SCIENCES / HeLa cells / Oxidative phosphorylation / Protein Biosynthesis / Mice / Animals / Tandem Mass Spectrometry / Biochemical / Phenotype / CHEMICAL SCIENCES / HeLa cells / Oxidative phosphorylation / Protein Biosynthesis
Mitochondrial gene expression and respiratory enzyme activities in cardiac diseases
Mitochondria / Gene expression / Biological Sciences / Mitochondrial DNA / Humans / Aortic stenosis / Female / Male / Physical sciences / Cytochrome c oxidase / Enzyme / Steady state / Clinical Sciences / Middle Aged / Oxidative phosphorylation / Multienzyme complexes / Enzyme activity / Pressure Gradient / Cardiac Disease / Biochemistry and cell biology / Heart Diseases / Aortic stenosis / Female / Male / Physical sciences / Cytochrome c oxidase / Enzyme / Steady state / Clinical Sciences / Middle Aged / Oxidative phosphorylation / Multienzyme complexes / Enzyme activity / Pressure Gradient / Cardiac Disease / Biochemistry and cell biology / Heart Diseases
Entacapone, a novel catechol-O-methyltransferase inhibitor for Parkinson\'s disease, does not impair mitochondrial energy production
Kinetics / Enzyme Inhibitors / Mitochondria / Energy Metabolism / Cell Culture / Cell line / Nitriles / Mice / Female / Animals / Male / Heart / European / Energy Production / Rats / Oxidative phosphorylation / Guinea Pig / Catechols / Wistar Rats / Oxygen Consumption / Cardiac function / Cell line / Nitriles / Mice / Female / Animals / Male / Heart / European / Energy Production / Rats / Oxidative phosphorylation / Guinea Pig / Catechols / Wistar Rats / Oxygen Consumption / Cardiac function
Inhibition of Mitochondrial Oxidative Phosphorylation Induces Hyper-Expression of Glutamic Acid Decarboxylase in Pancreatic Islet Cells
Immunology / Immunohistochemistry / Autoimmunity / Mitochondria / Insulin / Mice / Animals / Haloperidol / Oxidative phosphorylation / Arginine / Rodenticides / Type 2 Diabetes Mellitus / Furans / Cytotoxins / Glutamate decarboxylase / Radioimmunoassay / islets of Langerhans / Dopamine antagonists / Pancreatic islets / Mice / Animals / Haloperidol / Oxidative phosphorylation / Arginine / Rodenticides / Type 2 Diabetes Mellitus / Furans / Cytotoxins / Glutamate decarboxylase / Radioimmunoassay / islets of Langerhans / Dopamine antagonists / Pancreatic islets
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